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KMID : 0359719940120030484
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Journal of the Korean Neurological Association
1994 Volume.12 No. 3 p.484 ~ p.490
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Conduction Block in Hereditary Motor Sensory Neuropathy
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권기한
김성민/유경호/김상윤/이병철/최영철
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Abstract
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Electrodiagnostic features are particularly useful in distinguishing chronic acquired demyelinating neuropathy from familial demyelinating neuropathy. The electrodiagnostic findings in patients with familial demyelinating neuropathy reveal
uniform
solwing of NCV (nerve conduction velocity) in all the segments of nerve without conduction blocd. In contrast acquired group shows nonuniform slowing of NCV with temporal dispersion of CMAP (compound muscle action potential) on proximal
stimulation. In
addition conduction block in noted in some of acquired patients. We experienced 2 patients from one family with HSMN type I, who showed conduction block and concluded that differentiation between chronic acquired and familial demyelination
neuropathy is
not possible with conduction block alone in a substantial number of patients.
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KEYWORD
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